| 1 | CLPP, ERAL1
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| CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels.
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| Szczepanowska K, Maiti P, Kukat A, Hofsetz E, Nolte H, Senft K, Becker C, Ruzzenente B, Hornig-Do HT, Wibom R, Wiesner RJ, Krüger M, Trifunovic A.
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| EMBO J 35(23):2566-2583. Epub 2016 Oct 20.
2016
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| 2 | CLPP, PRLTS3
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| Perrault Syndrome Is Caused by Recessive Mutations in CLPP, Encoding a Mitochondrial ATP-Dependent Chambered Protease.
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| Jenkinson EM, Rehman AU, Walsh T, Clayton-Smith J, Lee K, Morell RJ, Drummond MC, Khan SN, Naeem MA, Rauf B, Billington N, Schultz JM, Urquhart JE, Lee MK, Berry A, Hanley NA, Mehta S, Cilliers D, Clayton PE, Kingston H, Smith MJ, Warner TT; University of Washington Center for Mendelian Genomics, Black GC, Trump D, Davis JR, Ahmad W, Leal SM, Riazuddin S, King MC, Friedman TB, Newman WG.
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| Am J Hum Genet 92(4):605-13. doi: 10.1016/j.ajhg.2013.02.013. Epub 2013 Mar 28.
2013
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| 3 | CLPP
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| Structures of ClpP in complex with acyldepsipeptide antibiotics reveal its activation mechanism.
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| Lee BG, Park EY, Lee KE, Jeon H, Sung KH, Paulsen H, Rübsamen-Schaeff H, Brötz-Oesterhelt H, Song HK.
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| Nat Struct Mol Biol 17(4):471-8. doi: 10.1038/nsmb.1787. Epub 2010 Mar 21.
2010
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| 4 | CLPP, FRDA, LONP1
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| Frataxin deficiency causes upregulation of mitochondrial Lon and ClpP proteases and severe loss of mitochondrial Fe-S proteins.
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| Guillon B, Bulteau AL, Wattenhofer-Donzé M, Schmucker S, Friguet B, Puccio H, Drapier JC, Bouton C.
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| FEBS J 276(4):1036-47. doi: 10.1111/j.1742-4658.2008.06847.x. Epub 2008 Jan 12.
2009
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| 5 | CLPP
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| The ClpP N-terminus coordinates substrate access with protease active site reactivity.
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| Jennings LD, Bohon J, Chance MR, Licht S.
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| Biochemistry 47(42):11031-40. doi: 10.1021/bi8010169. Epub 2008 Sep 25.
2008
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| 6 | CLPP
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| Human mitochondrial ClpP is a stable heptamer that assembles into a tetradecamer in the presence of ClpX.
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| Kang SG, Dimitrova MN, Ortega J, Ginsburg A, Maurizi MR.
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| J Biol Chem 280(42):35424-32. Epub 2005 Aug 22. 2005
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| 7 | CLPP
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| Mitochondrial localization and oligomeric structure of HClpP, the human homologue of E. coli ClpP.
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| de Sagarra MR, Mayo I, Marco S, Rodriguez-Vilarino S, Oliva J, Carrascosa JL, Casta n JG.
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| J Mol Biol 292(4):819-25 1999
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| 8 | CLPP
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| A human homologue of Escherichia coli ClpP caseinolytic protease: recombinant expression, intracellular processing and subcellular localization.
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| Corydon TJ, Bross P, Holst HU, Neve S, Kristiansen K, Gregersen N, Bolund L.
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| Biochem J 331 ( Pt 1):309-16. 1998
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| 9 | CLPP
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| Human ClpP protease : cDNA sequence, tissue-specific expression and chromosomal assignment of the gene.
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| Bross P, et al.
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| FEBS Lett 377 : 249-252. 1995
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