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GENATLAS PHENOTYPE

last update : 17-11-2015

Symbol	OLD2
Location	6q27
Name	oligodontia 2
Other name(s)	Dentin dysplasia, type I
Corresponding gene	SMOC2
Other symbol(s)	DTDP1
Main clinical features	extreme microdontia, oligodontia, dental shape anomalies, double permanent-tooth formation, thin enamel, and short roots (with a thin associated alveolar bone), as seen in the spectrum of dentin dysplasia type I primary teeth were mobile and exfoliated prematurely
Genetic determination	autosomal recessive
Function/system disorder	dermatology
Type	disease

Remark(s)