| Main clinical features
|
congenital deformity manifesting as an abnormally shaped or absent external ear, with a small, abnormally shaped outer ear
lobule, helix, and anti-helix, are present in grade I, the external ear is smaller than normal
in grade II, the normal features of the external ear are absent ; a lobule, a helix, and an anti-helix are present, but they are small and not well formed
in grade III, the external ear consists of a vertical skin appendage with a malformed lower end of the ear lobe
no external ear or auditory canal is called anotia, or microtia grade IV |