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References OMIM Gene GeneReviews HGMD HGNC
last update : 14-02-2011
Symbol LQT4
Location 4q26
Name long QT syndrome with ventricular tachyarrhythmia, type 4
Other name(s) sick sinus syndrome with bradycardia
Corresponding gene ANK2
Main clinical features
  • syncopes, seizures predisposing to torsades de pointes, ventricular fibrillation and sudden death
  • sinus node disease, conduction defects, ventricular arrhythmia, and sudden death (PMID: 20610380))
  • Genetic determination autosomal dominant
    Function/system disorder cardiovascular
    Type disease
    Gene product
    Name ankyrin 2, neuronal