| Symbol
| IDMS
|
| Location
| 11p13
|
| Name
|
nephrotic syndrome with an isolated diffuse or, rarely, a focal segmental mesangial sclerosis |
| Other name(s)
|
mesangial sclerosis, familial
mesangial sclerosis, isolated diffuse |
| Corresponding gene
|
WT1
|
| Other symbol(s)
| DMS
|
| Main clinical features
|
onset in infancy of asymptomatic proteinuria with subsequent development of the nephrotic syndrome and progression to renal failure and death before the age of 3 years, at renal histopathology, infantile mesangial sclerosis |
| Genetic determination
| autosomal recessive |
| Function/system disorder
| kidney and urinary tract |
| Type
| disease
|