Main clinical features
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proliferative lesions within the mandible and maxilla with loss of bone in the jaws and its replacement with large amounts of fibrous tissue, multinuceated giant cells
begins around the third or fourth year of life and progresses until the late teens
facial disfigurement, early tooth loss, failure of permanent tooth eruption, and distortion of the orbital socket creating an upturned eye appearance occasionally associated with blindness
at radiography, multilocular cystic changes in the mandible and maxilla and often in the anterior ends of the ribs |