Selected-GenAtlas references SOURCE GeneCards NCBI Gene Swiss-Prot Orphanet Ensembl
HGNC UniGene Nucleotide OMIM UCSC
Home Page
FLASH GENE
Symbol HIBCH contributors: KTN/npt - updated : 18/09/2008
HGNC name 3-hydroxyisobutyryl-Coenzyme A hydrolase
HGNC id 4908
PROTEIN
PHYSICAL PROPERTIES
STRUCTURE
motifs/domains
mono polymer homomer , hexamer
HOMOLOGY
interspecies homolog to dog HIBCH (90.8 pc)
homolog to chimpanzee HIBCH (99.7 pc)
homolog to rattus Hibch (79.4 pc)
homolog to murine Hibch (82.1 pc)
homolog to chicken HIBCH (70.9 pc)
Homologene
FAMILY
  • enoyl-coa hydratase/isomerase family
  • CATEGORY enzyme
    SUBCELLULAR LOCALIZATION     intracellular
    intracellular,cytoplasm,organelle,mitochondria,matrix
    intracellular,nucleus
    basic FUNCTION
  • hydrolyzing 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite and 3-hydroxypropanoyl-CoA
  • could be an isobutyryl-CoA dehydrogenase functioning in valine catabolism
  • CELLULAR PROCESS
    PHYSIOLOGICAL PROCESS
    PATHWAY
    metabolism aminoacid
    signaling
    L-valine catabolism
    a component
    INTERACTION
    DNA
    RNA
    small molecule
    protein
    cell & other
    REGULATION
    ASSOCIATED DISORDERS
    corresponding disease(s) HIBCHD
    Susceptibility
    Variant & Polymorphism
    Candidate gene
    Marker
    Therapy target
    ANIMAL & CELL MODELS